Uterus Didelphys With Bilateral Cervical Agenesis

Authors

  • Dwinda Rizary Resident of Obstetrics and Gynecology, Faculty of Medicine, Andalas University, Dr. M. Djamil Central General Hospital Padang
  • Dedy Hendry Sub Division of Reproductive Endocrinology, Obstetrics and Gynecology Department, Faculty of Medicine, Andalas University, Dr. M. Djamil Central General Hospital Padang

DOI:

https://doi.org/10.25077/aoj.4.1.133-138.2020

Abstract

Background : The mullerian duct anomaly is a congenital abnormality of the female reproductive system caused by abnormal embryological development during pregnancy. If accompanied by cervical agenesis and infertility, intervention must be taken. Accurate diagnosis and proper treatment are very crucial to the future of reproduction and treatment of infertility in patients.

Objective: Reporting the handling of cases of uterine didelphys accompanied by bilateral cervical agenesis.

Method : Case report

Case: Reported cases of women aged 34 years with primary amenorrhea and 9 years primary infertility, not typical cyclic pain, normal secondary sex development and from gynecological examination obtained cervical agenesis. Transvaginal ultrasound examination found a mass with the appearance of adenomyosis. Laparoscopic performed show 2 masses, 1 mass resembling adenomyosis with a size of 9x6x5cm located lateral to the left pelvis and another mass in the form of a hypoplastic uterus with a size of 2x2x1cm visible 2 tubes with 2 ovaries within normal limits. Uterine mass resembling adenomyosis with a location far from the vagina making it difficult to do anastomoses while other uterus hypoplasia and non-functional. Hysterectomies were performed on the mass of adenomyosis with the results of PA was adenomyosis.

Conclusion: The uterus didelphys with bilateral cervical agenesis with 1 uterine adenomyosis and located in the pelvic lateral it was difficult to do uterovaginal anastomose so that hysterectomy was performed. Second uterine was hypoplasia and non-functional so that no action was taken. Need to think about "future fertility" in these patients and various options for having children.

Keywords: Primary Amenorrhea, Uterine Didelphys, Cervical Agenesis, Adenomyosis

References

Parikh, R., et al. (2013). "Mullerian anomalies: a cause of primary amenorrhea." International Journal of Reproduction, Contraception, Obstetrics and Gynecology: 393-397.

Boehnke, M., et al. (2016). "Uterine didelphys with concomitant renal anomalies in both mother and fetus." Journal of Pediatric Surgery Case Reports 14: 19-21.

Acien, P., et al. (2009). "Mullerian anomalies "without a classification": from the didelphys-unicollis uterus to the bicervical uterus with or without septate vagina." Fertil Steril 91(6): 2369-2375.

Helmy, Y. A. (2017). "Cervical agenesis with a functioning uterus: Successful surgical treatment by Foley’s catheter stent: A case report." Middle East Fertility Society Journal 22(1): 67-69.

Fritz M, Sperrof L. Clinical Gynecologi endocrinoloy and Infertility 8 th edition. Lippicort WiliiamWillims. USA; 2011.

Haydardedeoglu, B. and P. Caglar Aytac (2016). "A novel approach for congenital absence of the uterine cervix: Office hysteroscopic versapoint canalization using real-time trans-abdominal sonography guidance." Turk J Obstet Gynecol 13(1): 42-45.

Yoshiki, N., et al. (2008). "Unusual uterus didelphys presenting in the retroperitoneum." Fertil Steril 90(2): 427-428.

Lakshmy, S. and N. Rose (2016). "Congenital absence of uterine cervix." International Journal of Reproduction, Contraception, Obstetrics and Gynecology: 3634-3636.

Adair, L., 2nd, et al. (2011). "Uterus didelphys with unilateral distal vaginal agenesis and ipsilateral renal agenesis: common presentation of an unusual variation." J Radiol Case Rep 5(1): 1-8.

Arnold, K. C., et al. (2018). "Uterine Didelphys with Bilateral Cervical Agenesis in a 15-Year-Old Girl." J Pediatr Adolesc Gynecol 31(1): 64-66.

Mahmud, Nusrat, et al.(2014). “Successful Uterovaginal Anastomosis in An Unusual Presentation of Congenital Absence of Cervix.†J. South Asian Federation Of Menopause : 105-110

Downloads

Published

2020-01-10

Issue

Vol 4, No 1 (2020)

Section

CASE REPORT

License

Copyright (c) 2020 JOURNAL OBGIN EMAS

Creative Commons License

This work is licensed under a Creative Commons Attribution 4.0 International License.

Copyright

Authors who publish with this journal agree to the following terms:

  1. Authors retain the copyright of published articles and grant the journal right of first publication with the work simultaneously licensed under a Creative Commons Attribution 4.0 International License that allows others to share the work with an acknowledgment of the work's authorship and initial publication in this journal.
  2. Authors are able to enter into separate, additional contractual arrangements for the non-exclusive distribution of the journal's published version of the work (e.g., post it to an institutional repository or publish it in a book), with an acknowledgment of its initial publication in this journal.
  3. Authors are permitted and encouraged to post their work online (e.g., in institutional repositories or on their website) prior to and during the submission process, as it can lead to productive exchanges, as well as earlier and greater citation of published work (See The Effect of Open Access).

License:

Andalas Obstetrics and Gynecology Journal (AOJ) is published under the terms of the Creative Commons Attribution 4.0 International License. This license permits anyone to copy and redistribute this material in any form or format, compose, modify, and make derivatives of this material for any purpose, including commercial purposes, as long as they credit the author for the original work.